EB Statistics

 

EB Statistics

The incidence column is the one that estimates number born in a given year. The last official birthrate numbers are form 2009, and that year it was 4,130,665 (2010 and 2011 are not available)

Material is based on the NEBR study population 

EB type or subtype:	Prevalence*	Incidence**
EB (All types and subtypes, including unclassified patients)	8.22	19.60
EBS	4.60	10.75
EBS, Localized (formerly Weber- Cockayne)	3.14	6.81
EBS, all others	1.46	3.95
JEB	0.44	2.40
JEB-Herlitz	0.07	<0.41
JEB, other	0.37	<2.04
DDEB	0.99	2.86
RDEB	0.92	2.04
RDEB, severe generalized (formerly Hallopeau- Siemens)	0.42	0.41
RDEB, all others	0.49	1.63

*Prevalence of EB patients per one million births (1990)

**Incidence of EB births per one million live births (1986-1990)

Fine, Jo-David and Hintner, Helmut. (2008) "Life with Epidermolysis Bullosa (EB): Etilogy, Diagnosis, Multidisciplinary Care and Therapy" Springer-Verlag/Wien, New York. 

The number in the Incidence Column is per 1 million births so to find the actual number of new cases of EB each year in the US, multiple that number by 4.13 (the approximate total number of births in the US each year)

So there is approximately 80 new cases of EB in the US each year.  Of those 80- 

45 will have some form of EB Simplex

10 will have some form of Junctional

12 will have Dominant Dystrophic EB

10 will have Recessive Dystrophic EB

This is just an approximate # and some years there will be more or less in each category. 

©Garrett's House 2021